红细胞生成性卟啉病
- 网络erythropoietic porphyria;Cep
红细胞生成性卟啉病
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目的研究和比较先天性红细胞生成性卟啉病(CEP)患者、迟发性皮肤卟啉病(PCT)患者和正常健康者的红细胞酶活性。
Objective To study and compare the enzyme activities of erythrocyte in Congenital erythropoietic porphyrias ( CEP ), Porphyria cutanea tardas ( PCT ) and healthy normals subjects .
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国产β-胡萝卜素治疗红细胞生成性原卟啉病
β - carotene therapy for erythropoietic protoporphyria
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采用临床对照试验观察口服β-胡萝卜素治疗红细胞生成性原卟啉病的光敏反应,治疗组33例,显效率为60%,总有效率100%。
In a controlled clinical study , oral β - carotene was used to reduce the severity of photosensitivity reactions in patients with erythropoietic protoporphyria . Out of 33 cases treated with β - carotene , 60 % showed significant response , and total response rate was 100 % .